Biventricular Non-Compaction Cardiomyopathy

A 48-year-old male was referred for ultrasound evaluation after experiencing shortness of breath and atrial flutter—common symptoms with an uncommon cause. Imaging revealed heart failure secondary to biventricular non-compaction cardiomyopathy, a rare and often underdiagnosed condition affecting the heart’s muscle structure.

Management includes medications such as ACE inhibitors or ARBs, beta-blockers, diuretics, and devices like pacemakers, implantable cardioverter-defibrillators (ICDs), or cardiac resynchronization therapy (CRT). In severe cases, while a patient is awaiting a heart transplant, a ventricular assist device (R/L-VAD) may be required. Ongoing care emphasizes adopting a heart-healthy lifestyle and maintaining regular follow-ups with a dedicated care team.

This case underscores the value of high-quality ultrasound as a diagnostic tool and a clinical compass, guiding immediate and long-term care. By detecting a rare and potentially life-threatening condition, the BB Imaging team played a crucial role in enabling immediate case management, thereby reducing the risk of further complications and setting the stage for sustainable symptom and medication management.